Definition

Midline arteriovenous fistulae with aneurysmal dilatation of the vein of Galen.

Clinical presentation

The most common presenting symptoms in newborns include:

Condition	Frequency
Congestive cardiac failure	47%
Raised intracranial pressure secondary to hydrocephalus	40%
Cranial bruit	25%
Focal neurological deficit	16%
Seizures	11%
Hemorrhage	10%